Peter Olejník, Jozef Mašura
Introduction: Pulmonary atresia with ventricular septal defect and multiple aortopulmonary collaterals is a complex cyanotic congenital heart defect with severe prognosis. Because of complex anatomy of the defect, there was no chirurgical intervention indicated in the past. These days, there are several chirurgical procedures and interventional methods used in the therapeutic managment of patients with pulmonary atresia with ventricular septal defect and multiple aortopulmonary collaterals. Goal: Complex explanation of diagnosis pulmonary atresia with ventricular septal defect and multiple aortopulmonary collaterals for general pediatricians. A comparision of survival and incidence of complication requiring surgical intervention or invasive cathetrization between groups of operated and non-operated patients. Methods: Retrospecive and prospective analysis of group of patients with diagnosis of PA, VSD and MAPCAs born in 1981 - 2004 in Slovakia. Results: Increased survival in the group of operated patients in comparision to group of non-operated patients (88 %/81 % – in correlation to 9th survived year of life) and very often neccesity of surgical intervention or invasive cathetrization in the group of operated patients (47 % of operated patients).