Vladimír Bartoš, Dušan Pokorný, Juraj Mikuláš, Barbora Škripeková
Splenogonadal fusion (SGF) is a very rare congenital malformation in which there is an abnormal connection between
the spleen and the gonad or derivatives of the mesonephros. Conventionally, it is classified as a continuous and discontinuous
type. The authors describe a case report of a nearly 16-year old boy, who underwent a left-sided orchiectomy
because of the hypoplastic testis. Grossly, a separate pedunculated ovoid structure up to 17 mm attached to the tunica
vaginalis was also found. Histologically, it was an accessory spleen consisted of physiologically developed white and red
pulp. In the testicle, seminiferous tubules contained only Sertoli cells without evidence of spermiogenesis. The pathologic
finding was in line with a diagnosis of the discontinuous type of SGF with testicular hypoplasia. In routine clinical
practice, SGF represents a unique congenital anomaly. In boys, it is often associated with an undescended testis or an
inguinal hernia. Despite the rarity, this nosologic entity should be included in the differential diagnostic approach of intrascrotal
pathological masses, especially in children.