Monika Kaldarárová1, Andrea Kántorová1, Zuzana Berecová2, Iveta Šimková3
Tetralogy of Fallot is one of the most frequent cyanotic congenital heart defects. Due to good surgical results more and more patients reach adulthood. This defect is though, even after complete correction, not definitely repaired but brings up the risk of late complications and so needs lifelong follow-up. The most frequent problem represents severe pulmonary regurgitation cau-sing chronic right ventricular volume overload that has to be attended before ventricular dysfunction or failure occurs. Further considerable findings may be residual pulmonary stenosis, hemodynamically significant ventricular septal defect and ascending aorta dilatation and/or aortic regurgitation. Risk factor may be also the presence of arrhythmias that represent the most frequent cause of sudden cardiac death in patients after complete correction of tetralogy of Fallot. This work analyses the causes and importance of particular complications, proposes diagnostic algorithms, up-to-date indication criteria for re-intervention and optimal long-term management of these patients.